TY  - JOUR
AU  - Oller, Jorge
AU  - Gabandé-Rodríguez, Enrique
AU  - Ruiz-Rodríguez, María Jesús
AU  - Desdín-Micó, Gabriela
AU  - Aranda, Juan Francisco
AU  - Rodrigues-Diez, Raquel
AU  - Ballesteros-Martínez, Constanza
AU  - Blanco, Eva María
AU  - Roldan-Montero, Raquel
AU  - Acuña, Pedro
AU  - Forteza Gil, Alberto
AU  - Martín-López, Carlos E
AU  - Nistal, J Francisco
AU  - Lino Cardenas, Christian L
AU  - Lindsay, Mark Evan
AU  - Martín-Ventura, José Luís
AU  - Briones, Ana M
AU  - Redondo, Juan Miguel
AU  - Mittelbrunn, María
PY  - 2021
DO  - 10.1161/CIRCULATIONAHA.120.051171
UR  - http://hdl.handle.net/20.500.12105/15405
AB  - Marfan syndrome (MFS) is an autosomal dominant disorder of the connective tissue caused by mutations in the FBN1 (fibrillin-1) gene encoding a large glycoprotein in the extracellular matrix called fibrillin-1. The major complication of this connective...
LA  - eng
PB  - American Heart Association (AHA)
KW  - Animals
KW  - Aortic Aneurysm
KW  - Disease Models, Animal
KW  - Humans
KW  - Marfan Syndrome
KW  - Mice
KW  - Mitochondria
TI  - Extracellular Tuning of Mitochondrial Respiration Leads to Aortic Aneurysm.
TY  - journal article
ER  -